Hereditary Benign Erythroreticulosis
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چکیده
I N THE PROVINCE of V#{228}sterbotten, Ncrth Sweden, we have observed a hitherto undescribed anomaly of erythropoiesis, characterized by : ( 1 ) a nonhemolytic normochromic anemia with a low or normal reticulocyte count and without indications of reduced activity of either granulocytopoiesis or thrombocytopoiesis; ( 2 ) a characteristic bone marrow picture, corresponding to that seen in the di Guglielmo disorder of erythremic myelosis;7 ( 3) an abnormal hemoglobin in the red blood cells; ( 4 ) a benign clinical course, but refractory to therapy; ( 5 ) a hereditary component. The reports of the first two cases are briefly summarized below:
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Hereditary Benign Erythroreticulosis
I N THE PROVINCE of V#{228}sterbotten, Ncrth Sweden, we have observed a hitherto undescribed anomaly of erythropoiesis, characterized by : ( 1 ) a nonhemolytic normochromic anemia with a low or normal reticulocyte count and without indications of reduced activity of either granulocytopoiesis or thrombocytopoiesis; ( 2 ) a characteristic bone marrow picture, corresponding to that seen in the di ...
متن کاملHereditary Benign Erythroreticulosis
I N THE PROVINCE of V#{228}sterbotten, Ncrth Sweden, we have observed a hitherto undescribed anomaly of erythropoiesis, characterized by : ( 1 ) a nonhemolytic normochromic anemia with a low or normal reticulocyte count and without indications of reduced activity of either granulocytopoiesis or thrombocytopoiesis; ( 2 ) a characteristic bone marrow picture, corresponding to that seen in the di ...
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